Clear cell papillary renal cell carcinoma (CCPRCC) is a newly recognized entity in the 2016WHOclassification and usually presents\nas a small, circumscribed, solitary mass of indolent nature. CCPRCCs could seldom occur in conjunction with other synchronous\nor metachronous kidney tumors and even less frequently as bilateral masses. To our knowledge, multiple bilateral CCPRCCs have\nnever been described with the existence of a synchronous well-differentiated neuroendocrine tumor of the kidney and hence\nreported here as a unique case. This case report highlights the importance in considering this entity and its unusual presentation\nin the differential diagnosis as a possible mimicker of Von Hippel-Lindau syndrome.
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